LDB2

Chr 4

LIM domain binding 2

Also known as: CLIM1, LDB-2, LDB1

The encoded protein functions as a transcription cofactor that binds to LIM domain-containing transcription factors, enabling assembly of transcriptional regulatory complexes. This gene is highly constrained against loss-of-function variants (pLI 0.95, LOEUF 0.34), but no established Mendelian diseases have been definitively linked to LDB2 mutations in current clinical practice. Genetic association studies have suggested potential roles in retinal detachment and coronary artery disease, though these represent complex trait associations rather than monogenic disorders.

Summary from RefSeq, UniProt
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0
Active trials
11
Pubs (1 yr)
0
P/LP submissions
P/LP missense
0.34
LOEUF· LoF intol.
LOF
Mechanism· predicted
Clinical SummaryLDB2
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 0.95). One damaged copy is likely sufficient to cause disease.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.34LOEUF
pLI 0.955
Z-score 3.56
OE 0.11 (0.040.34)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
2.37Z-score
OE missense 0.55 (0.470.64)
118 obs / 216.1 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.11 (0.040.34)
00.351.4
Missense OE0.55 (0.470.64)
00.61.4
Synonymous OE0.96
01.21.6
LoF obs/exp: 2 / 18.5Missense obs/exp: 118 / 216.1Syn Z: 0.32
DN
0.4686th %ile
GOF
0.3094th %ile
LOF
0.76top 10%

The highest-scoring mechanism for this gene is loss-of-function (haploinsufficiency).

LOFprediction above median · LOEUF 0.34

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

LDB2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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