LAMTOR3

Chr 4

late endosomal/lysosomal adaptor, MAPK and MTOR activator 3

Also known as: MAP2K1IP1, MAPBP, MAPKSP1, MP1, PRO0633, Ragulator3

This gene encodes a scaffold protein that functions in the extracellular signal-regulated kinase (ERK) cascade. The protein is localized to late endosomes by the mitogen-activated protein-binding protein-interacting protein, and binds specifically to MAP kinase kinase MAP2K1/MEK1, MAP kinase MAPK3/ERK1, and MAP kinase MAPK1/ERK2. Studies of the orthologous gene in mouse indicate that it regulates late endosomal traffic and cell proliferation. Alternatively spliced transcript variants encoding multiple isoforms have been observed for this gene. A pseudogene of this gene is located on the long arm of chromosome 13. [provided by RefSeq, Aug 2011]

OMIMResearchGenerating clinical summary…

Clinical highlights

Interpreting a novel variant
This gene is strongly intolerant of loss-of-function variation in the population, so LoF variants warrant close attention. No curated mechanism annotation is available — see the mechanism card for the computational prediction and its caveats.Based on population constraint only.
0
Active trials
6
Pubs (1 yr)
P/LP submissions
P/LP missense
0.55
LOEUF
Mechanism

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint?
0.55LOEUF
pLI 0.731
Z-score 2.41
OE 0.12 (0.040.55)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint?
0.04Z-score
OE missense 0.98 (0.801.22)
58 obs / 59.0 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.12 (0.040.55)
00.351.4
Missense OE?0.98 (0.801.22)
00.61.4
Synonymous OE?0.54
01.21.6
LoF obs/exp: 1 / 8.7Missense obs/exp: 58 / 59.0Syn Z: 1.62

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

LAMTOR3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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