KRT2

Chr 12AD

keratin 2

Also known as: CK-2e, K2e, KRT2A, KRT2E, KRTE

The protein encoded by this gene is a member of the keratin gene family. The type II cytokeratins consist of basic or neutral proteins which are arranged in pairs of heterotypic keratin chains coexpressed during differentiation of simple and stratified epithelial tissues. This type II cytokeratin is expressed largely in the upper spinous layer of epidermal keratinocytes and mutations in this gene have been associated with bullous congenital ichthyosiform erythroderma. The type II cytokeratins are clustered in a region of chromosome 12q12-q13. [provided by RefSeq, Jul 2008]

OMIMResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

Ichthyosis bullosa of SiemensMIM #146800
AD

Clinical highlights

Interpreting a novel variant
Loss of function is the curated mechanism (Gene2Phenotype), though the gene is not strongly LoF-constrained in the population — weigh truncating variants against that tolerance.Curated gene-level mechanism — a prior for triage, not a per-variant call.
0
Active trials
17
Pubs (1 yr)
P/LP submissions
P/LP missense
0.67
LOEUF
LOF*
Mechanism· G2P

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.67LOEUF
pLI 0.001
Z-score 2.77
OE 0.38 (0.230.67)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
-0.76Z-score
OE missense 1.11 (1.021.21)
400 obs / 359.4 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?0.38 (0.230.67)
00.351.4
Missense OE?1.11 (1.021.21)
00.61.4
Synonymous OE?1.30
01.21.6
LoF obs/exp: 9 / 23.4Missense obs/exp: 400 / 359.4Syn Z: -2.77

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

KRT2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →