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KRABD1

Chr 3

KRAB domain containing 1

Also known as: KRBOX1

The protein is predicted to regulate DNA-templated transcription. Currently, no well-established Mendelian diseases have been definitively linked to KRABD1 mutations in clinical practice. The clinical significance of variants in this gene remains to be determined.

ResearchSummary from RefSeq
Clinical SummaryKRABD1
📋
ClinVar Variants
5 unique Pathogenic / Likely Pathogenic of 7 total submissions
Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/KRABD1?content-type=application/json&expand=1

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

7 submitted variants in ClinVar

Classification Summary

Pathogenic4
Likely Pathogenic1
4
Pathogenic
1
Likely Pathogenic

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories· variant type breakdown unavailable

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
4
Likely Pathogenic
1
VUS
0
Likely Benign
0
Benign
0
Total5

Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

KRABD1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →

No publications found for KRABD1