KIF1C

Chr 17AR

kinesin family member 1C

Also known as: LTXS1, SATX2, SAX2, SPAX2, SPG58

KIF1C encodes a kinesin motor protein required for retrograde transport of Golgi vesicles to the endoplasmic reticulum and has microtubule plus end-directed motility. Mutations cause spastic ataxia 2, an autosomal recessive disorder affecting the central nervous system with both spasticity and ataxia features. The gene shows significant constraint against loss-of-function variants (LOEUF 0.341), suggesting intolerance to protein disruption.

OMIMResearchSummary from RefSeq, OMIM, UniProt
ARLOEUF 0.341 OMIM phenotype
Clinical SummaryKIF1C
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.72) — some intolerance to loss-of-function variants.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.34LOEUF
pLI 0.718
Z-score 5.52
OE 0.21 (0.130.34)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
1.40Z-score
OE missense 0.85 (0.790.91)
585 obs / 688.5 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.21 (0.130.34)
00.351.4
Missense OE0.85 (0.790.91)
00.61.4
Synonymous OE1.10
01.21.6
LoF obs/exp: 12 / 57.0Missense obs/exp: 585 / 688.5Syn Z: -1.29

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

KIF1C · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 5 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC