KIF14

Chr 1AR

kinesin family member 14

Also known as: MCPH20, MKS12

KIF14 encodes a microtubule motor protein with ATPase activity that is essential for cytokinesis, chromosome alignment during mitosis, and regulation of cell cycle progression. Mutations cause autosomal recessive primary microcephaly and Meckel syndrome, both reflecting severe developmental abnormalities with early onset. The gene is highly constrained against loss-of-function variants (LOEUF 0.429), consistent with its critical role in fundamental cellular processes including neurogenesis.

OMIMResearchSummary from RefSeq, OMIM, UniProt
LOFmechanismARLOEUF 0.432 OMIM phenotypes
Clinical SummaryKIF14
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.30) despite low pLI — interpret in context.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.43LOEUF
pLI 0.000
Z-score 5.63
OE 0.30 (0.220.43)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
0.77Z-score
OE missense 0.92 (0.870.98)
762 obs / 824.1 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.30 (0.220.43)
00.351.4
Missense OE0.92 (0.870.98)
00.61.4
Synonymous OE0.92
01.21.6
LoF obs/exp: 23 / 76.0Missense obs/exp: 762 / 824.1Syn Z: 1.01
Curated Mechanism (G2P)Gene2Phenotype (DDG2P) ↗
strongKIF14-related severe microcephaly and short statureLOFAR

Predictions shown for reference only — model trained on dominant genes, not applicable to AR conditions.

DN
0.75top 25%
GOF
0.5758th %ile
LOF
0.3648th %ile

The Badonyi & Marsh prediction model was trained exclusively on dominant disease genes. Predictions are not reliable for genes with autosomal recessive inheritance and are shown at reduced opacity for reference only.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

KIF14 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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