KIAA0319

Chr 6

KIAA0319

Also known as: DYLX2, DYX2, NMIG

This gene encodes a transmembrane protein that contains a large extracellular domain with multiple polycystic kidney disease (PKD) domains. The encoded protein may play a role in the development of the cerebral cortex by regulating neuronal migration and cell adhesion. Single nucleotide polymorphisms in this gene are associated with dyslexia. Alternatively spliced transcript variants encoding multiple isoforms have been observed for this gene. [provided by RefSeq, Nov 2011]

ResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtDyslexia 2
2
Active trials
10
Pubs (1 yr)
P/LP submissions
P/LP missense
0.99
LOEUF
DN
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.99LOEUF
pLI 0.000
Z-score 1.59
OE 0.76 (0.580.99)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
0.46Z-score
OE missense 0.95 (0.881.01)
567 obs / 598.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.76 (0.580.99)
00.351.4
Missense OE?0.95 (0.881.01)
00.61.4
Synonymous OE?0.88
01.21.6
LoF obs/exp: 37 / 49.0Missense obs/exp: 567 / 598.8Syn Z: 1.46

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

KIAA0319 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.