KHDC3L

Chr 6

KH domain containing 3 like, subcortical maternal complex member

Also known as: C6orf221, ECAT1, HYDM2

The protein encoded by this gene belongs to the KHDC1 family, members of which contain an atypical KH domain that may not bind RNA like canonical KH domains. This gene is specifically expressed in the oocytes, and recent studies suggest that it may function as a regulator of genomic imprinting in the oocyte. Mutations in this gene are associated with recurrent biparental complete hydatidiform mole. [provided by RefSeq, Dec 2011]

GeneReviewsResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtHydatidiform mole, recurrent, 2
0
Active trials
6
Pubs (1 yr)
P/LP submissions
P/LP missense
1.16
LOEUF
Multiple*
Mechanism· predicted
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GeneReview available — KHDC3L
Authoritative clinical overview · Recommended first read
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Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.16LOEUF
pLI 0.123
Z-score 1.36
OE 0.37 (0.151.16)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
0.20Z-score
OE missense 0.95 (0.831.10)
139 obs / 145.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.37 (0.151.16)
00.351.4
Missense OE?0.95 (0.831.10)
00.61.4
Synonymous OE?0.83
01.21.6
LoF obs/exp: 2 / 5.4Missense obs/exp: 139 / 145.7Syn Z: 1.06

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

KHDC3L · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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