KCNE5

Chr X

potassium voltage-gated channel subfamily E regulatory subunit 5

Also known as: KCNE1L

This gene encodes a member of a family of single pass transmembrane domain proteins that function as ancillary subunits to voltage-gated potassium channels. Members of this family affect diverse processes in potassium channel regulation, including ion selectivity, voltage dependence, and anterograde recycling from the plasma membrane. Variants of this gene are associated with idiopathic ventricular fibrillation and Brugada syndrome. [provided by RefSeq, Nov 2016]

GeneReviewsResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtAMME complex

Clinical highlights

Gene-disease validity (ClinGen)
Brugada syndrome · ADDisputedevidence questions this relationship
0
Active trials
3
Pubs (1 yr)
P/LP submissions
P/LP missense
1.83
LOEUF
Multiple*
Mechanism· predicted
📖
GeneReview available — KCNE5
Authoritative clinical overview · Recommended first read
Open GeneReview ↗
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.83LOEUF
pLI 0.119
Z-score 0.40
OE 0.65 (0.201.83)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
0.41Z-score
OE missense 0.86 (0.701.07)
60 obs / 69.5 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.65 (0.201.83)
00.351.4
Missense OE?0.86 (0.701.07)
00.61.4
Synonymous OE?0.72
01.21.6
LoF obs/exp: 1 / 1.5Missense obs/exp: 60 / 69.5Syn Z: 1.32

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

KCNE5 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →