JMJD8

Chr 16

jumonji domain containing 8

Also known as: C16orf20, PP14397

JMJD8 encodes a protein that regulates TNF-induced NF-kappaB signaling and controls angiogenesis and cellular metabolism through interaction with pyruvate kinase. Mutations cause autosomal recessive intellectual developmental disorder with seizures and language delay, with onset in early childhood. The gene shows low constraint against loss-of-function variants, consistent with recessive inheritance.

ResearchSummary from RefSeq, UniProt
LOEUF 1.81
Clinical SummaryJMJD8
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.81LOEUF
pLI 0.000
Z-score -0.95
OE 1.27 (0.881.81)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-1.92Z-score
OE missense 1.43 (1.281.60)
224 obs / 156.3 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE1.27 (0.881.81)
00.351.4
Missense OE1.43 (1.281.60)
00.61.4
Synonymous OE1.55
01.21.6
LoF obs/exp: 18 / 14.1Missense obs/exp: 224 / 156.3Syn Z: -3.61

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

JMJD8 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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