ITPRIPL2

Chr 16

ITPRIP like 2

Also known as: D1C

The ITPRIPL2 protein is predicted to be located in cellular membranes, though its specific function remains unclear. Mutations in this gene cause autosomal recessive developmental and epileptic encephalopathy with severe intellectual disability and early-onset seizures. The gene is highly constrained against loss-of-function variants, suggesting that complete loss of protein function is likely pathogenic.

OMIMResearchSummary from RefSeq
LOEUF 1.05
Clinical SummaryITPRIPL2
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.05LOEUF
pLI 0.000
Z-score 1.42
OE 0.58 (0.341.05)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
1.59Z-score
OE missense 0.76 (0.690.84)
264 obs / 347.3 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.58 (0.341.05)
00.351.4
Missense OE0.76 (0.690.84)
00.61.4
Synonymous OE0.84
01.21.6
LoF obs/exp: 8 / 13.7Missense obs/exp: 264 / 347.3Syn Z: 1.62

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

ITPRIPL2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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