IRX2-DT

Chr 5

IRX2 divergent transcript

Also known as: C5orf38, CEI, IRX2NB

IRX2-DT is a long non-coding RNA predicted to be located in the extracellular region, though its specific function remains unclear. No established disease associations have been reported for mutations in this gene based on the available information. The gene shows low constraint against loss-of-function variants, suggesting it may be tolerant to genetic variation.

OMIMResearchSummary from RefSeq
MultiplemechanismLOEUF 1.40
Clinical SummaryIRX2-DT
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.40LOEUF
pLI 0.002
Z-score 0.83
OE 0.67 (0.351.40)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.47Z-score
OE missense 1.15 (0.971.37)
91 obs / 79.2 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.67 (0.351.40)
00.351.4
Missense OE1.15 (0.971.37)
00.61.4
Synonymous OE1.22
01.21.6
LoF obs/exp: 5 / 7.4Missense obs/exp: 91 / 79.2Syn Z: -1.05
DN
0.6647th %ile
GOF
0.77top 25%
LOF
0.3552th %ile

This gene has evidence for multiple mechanisms of pathogenicity (gain-of-function and dominant-negative). Both the Badonyi & Marsh prediction and the broader genomic evidence point to gain-of-function as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

GOFprediction above median
DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

IRX2-DT · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found