INPP5K

Chr 17AR

inositol polyphosphate-5-phosphatase K

Also known as: MDCCAID, PPS, SKIP

This gene encodes a protein with 5-phosphatase activity toward polyphosphate inositol. The protein localizes to the cytosol in regions lacking actin stress fibers. It is thought that this protein may negatively regulate the actin cytoskeleton. Alternatively spliced transcript variants encoding different isoforms have been identified. [provided by RefSeq, Oct 2008]

OMIMResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

Muscular dystrophy, congenital, with cataracts and intellectual disabilityMIM #617404
AR
1
Active trials
7
Pubs (1 yr)
P/LP submissions
P/LP missense
0.79
LOEUF
Mechanism

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.79LOEUF
pLI 0.000
Z-score 2.34
OE 0.48 (0.300.79)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
0.60Z-score
OE missense 0.90 (0.811.00)
248 obs / 276.1 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.48 (0.300.79)
00.351.4
Missense OE?0.90 (0.811.00)
00.61.4
Synonymous OE?0.95
01.21.6
LoF obs/exp: 11 / 23.1Missense obs/exp: 248 / 276.1Syn Z: 0.47

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

INPP5K · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.