ING2

Chr 4

inhibitor of growth family member 2

Also known as: ING1L, ING1Lp, p33ING2

The ING2 protein functions as a component of histone acetyltransferase and histone deacetylase complexes, regulating chromatin modification and participating in DNA repair and p53-mediated apoptotic pathways. Mutations in ING2 cause autosomal dominant intellectual disability with behavioral abnormalities and seizures, typically presenting in early childhood. The gene shows moderate constraint against loss-of-function variants (pLI = 0.73, LOEUF = 0.48), suggesting intolerance to complete protein loss.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
5
Pubs (1 yr)
97
P/LP submissions
0%
P/LP missense
0.48
LOEUF
LOF
Mechanism· predicted
Clinical SummaryING2
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.73) — some intolerance to loss-of-function variants.
📋
ClinVar Variants
97 unique Pathogenic / Likely Pathogenic· 24 VUS of 121 total submissions
Some data sources returned errors (1)

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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.48LOEUF
pLI 0.729
Z-score 2.83
OE 0.15 (0.060.48)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
1.74Z-score
OE missense 0.59 (0.500.71)
87 obs / 146.2 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.15 (0.060.48)
00.351.4
Missense OE0.59 (0.500.71)
00.61.4
Synonymous OE0.92
01.21.6
LoF obs/exp: 2 / 13.0Missense obs/exp: 87 / 146.2Syn Z: 0.47
DN
0.4090th %ile
GOF
0.3094th %ile
LOF
0.72top 10%

The highest-scoring mechanism for this gene is loss-of-function (haploinsufficiency).

LOFprediction above median · LOEUF 0.48

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

121 submitted variants in ClinVar

Classification Summary

Pathogenic89
Likely Pathogenic8
VUS24
89
Pathogenic
8
Likely Pathogenic
24
VUS

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
89
0
89
Likely Pathogenic
0
0
8
0
8
VUS
0
18
6
0
24
Likely Benign
0
0
0
0
0
Benign
0
0
0
0
0
Total0181030121

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

ING2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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