IL17RC

Chr 3AR

interleukin 17 receptor C

Also known as: CANDF9, IL17-RL, IL17RL

This protein functions as a receptor for the proinflammatory cytokines IL-17A and IL-17F, activating NF-kappa-B signaling pathways that are essential for antimicrobial host defense and stimulating production of antimicrobial peptides by epithelial cells. Autosomal recessive mutations cause familial candidiasis, characterized by chronic mucocutaneous candidal infections due to impaired immune responses against fungal pathogens. The gene shows extremely low constraint against loss-of-function variants (pLI near zero), consistent with the recessive inheritance pattern where heterozygous carriers are typically unaffected.

OMIMResearchSummary from RefSeq, OMIM, UniProt
ARLOEUF 0.871 OMIM phenotype
Clinical SummaryIL17RC
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
13 unique Pathogenic / Likely Pathogenic· 296 VUS of 500 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.87LOEUF
pLI 0.000
Z-score 2.28
OE 0.64 (0.470.87)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
0.09Z-score
OE missense 0.99 (0.911.07)
441 obs / 446.5 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.64 (0.470.87)
00.351.4
Missense OE0.99 (0.911.07)
00.61.4
Synonymous OE1.11
01.21.6
LoF obs/exp: 29 / 45.6Missense obs/exp: 441 / 446.5Syn Z: -1.26

ClinVar Variant Classifications

500 submitted variants in ClinVar

Classification Summary

Pathogenic8
Likely Pathogenic5
VUS296
Likely Benign163
Benign2
Conflicting5
8
Pathogenic
5
Likely Pathogenic
296
VUS
163
Likely Benign
2
Benign
5
Conflicting

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
8
0
8
Likely Pathogenic
4
0
1
0
5
VUS
21
250
22
3
296
Likely Benign
0
2
66
95
163
Benign
0
0
2
0
2
Conflicting
5
Total252529998479

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

IL17RC · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC