IGSF6

Chr 16

immunoglobulin superfamily member 6

Also known as: DORA

The protein is predicted to function as a transmembrane signaling receptor involved in cell surface signaling pathways and immune responses. Mutations in this gene have not been definitively associated with human disease based on the available information. The gene shows low constraint against loss-of-function variants, suggesting it may be more tolerant to genetic variation.

OMIMResearchSummary from RefSeq
MultiplemechanismLOEUF 1.08
Clinical SummaryIGSF6
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.08LOEUF
pLI 0.001
Z-score 1.38
OE 0.55 (0.301.08)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.15Z-score
OE missense 0.96 (0.831.12)
129 obs / 133.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.55 (0.301.08)
00.351.4
Missense OE0.96 (0.831.12)
00.61.4
Synonymous OE1.02
01.21.6
LoF obs/exp: 6 / 10.9Missense obs/exp: 129 / 133.8Syn Z: -0.11
DN
0.74top 25%
GOF
0.6931th %ile
LOF
0.2189th %ile

This gene has evidence for multiple mechanisms of pathogenicity (dominant-negative and gain-of-function). Both the Badonyi & Marsh prediction and the broader genomic evidence point to dominant-negative as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

DNprediction above median
GOFprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

IGSF6 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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