IFT81

Chr 12

intraflagellar transport 81

Also known as: CDV-1, CDV-1R, CDV1, CDV1R, DV1, SRTD19

The protein encoded by this gene, together with IFT74, forms a tubulin-binding module of intraflagellar transport complex B. This module is involved in transport of tubulin within the cilium, and the encoded protein is required for ciliogenesis. Mutations in this gene are a cause of short-rib polydactyly syndromes. [provided by RefSeq, Dec 2016]

ResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtShort-rib thoracic dysplasia 19 with or without polydactyly

Clinical highlights

Gene-disease validity (ClinGen)
short-rib thoracic dysplasia 19 with or without polydactyly · ARModerateconsider for supplementary testing
0
Active trials
5
Pubs (1 yr)
P/LP submissions
P/LP missense
0.80
LOEUF
DN
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.80LOEUF
pLI 0.000
Z-score 2.63
OE 0.57 (0.410.80)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
0.83Z-score
OE missense 0.87 (0.790.96)
293 obs / 335.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.57 (0.410.80)
00.351.4
Missense OE?0.87 (0.790.96)
00.61.4
Synonymous OE?0.96
01.21.6
LoF obs/exp: 25 / 43.8Missense obs/exp: 293 / 335.7Syn Z: 0.29

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

IFT81 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →