IFT43

Chr 14AR

intraflagellar transport 43

Also known as: C14orf179, CED3, RP81, SRTD18

This gene encodes a subunit of the intraflagellar transport complex A (IFT-A). IFT-A is a multiprotein complex that plays an important role in cilia assembly and maintenance by mediating retrograde ciliary transport. Mutations in this gene are a cause of cranioectodermal dysplasia-3 (CED3), also known as Sensenbrenner syndrome. Alternatively spliced transcript variants encoding multiple isoforms have been observed for this gene. [provided by RefSeq, Dec 2011]

GeneReviewsOMIMResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

?Cranioectodermal dysplasia 3MIM #614099
AR
?Retinitis pigmentosa 81MIM #617871
AR
Short-rib thoracic dysplasia 18 with polydactylyMIM #617866
AR

Clinical highlights

Gene-disease validity (ClinGen)
ciliopathy · ARModerateconsider for supplementary testing
Interpreting a novel variant
Loss of function is the curated mechanism (Gene2Phenotype), though the gene is not strongly LoF-constrained in the population — weigh truncating variants against that tolerance.Curated gene-level mechanism — a prior for triage, not a per-variant call.
0
Active trials
6
Pubs (1 yr)
P/LP submissions
P/LP missense
1.60
LOEUF
LOF
Mechanism· G2P
📖
GeneReview available — IFT43
Authoritative clinical overview · Recommended first read
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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.60LOEUF
pLI 0.000
Z-score -0.21
OE 1.06 (0.721.60)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
-0.30Z-score
OE missense 1.08 (0.931.24)
132 obs / 122.8 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?1.06 (0.721.60)
00.351.4
Missense OE?1.08 (0.931.24)
00.61.4
Synonymous OE?1.18
01.21.6
LoF obs/exp: 16 / 15.1Missense obs/exp: 132 / 122.8Syn Z: -0.99

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

IFT43 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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