IER3IP1

Chr 18

immediate early response 3 interacting protein 1

Also known as: HSPC039, MEDS, PRO2309

This gene encodes a small protein that is localized to the endoplasmic reticulum (ER) and may play a role in the ER stress response by mediating cell differentiation and apoptosis. Transcription of this gene is regulated by tumor necrosis factor alpha and specificity protein 1 (Sp1). Mutations in this gene may play a role in microcephaly, epilepsy, and diabetes syndrome (MEDS), and a pseudogene of this gene is located on the long arm of chromosome 12. [provided by RefSeq, Dec 2011]

ResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtMicrocephaly, epilepsy, and diabetes syndrome 1
0
Active trials
6
Pubs (1 yr)
P/LP submissions
P/LP missense
1.41
LOEUF
Multiple*
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.41LOEUF
pLI 0.023
Z-score 0.95
OE 0.56 (0.251.41)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
-0.39Z-score
OE missense 1.17 (0.931.48)
50 obs / 42.8 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?0.56 (0.251.41)
00.351.4
Missense OE?1.17 (0.931.48)
00.61.4
Synonymous OE?1.37
01.21.6
LoF obs/exp: 3 / 5.4Missense obs/exp: 50 / 42.8Syn Z: -1.23

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

IER3IP1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →