IDLDP

Chr 2AD

nuclear receptor subfamily 4 group A member 2

Also known as: HZF-3, IDLDP, NOT, NURR1, RNR1, TINUR

The encoded protein is a transcription factor belonging to the steroid-thyroid hormone-retinoid receptor superfamily. Mutations cause intellectual developmental disorder with language impairment and early-onset DOPA-responsive dystonia-parkinsonism, inherited in an autosomal dominant pattern. This condition affects both neurodevelopmental and movement disorder domains, with dystonia-parkinsonism symptoms appearing in early life and showing responsiveness to DOPA therapy.

Summary from RefSeq, OMIM
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Primary Disease Associations & Inheritance

Intellectual developmental disorder with language impairment and early-onset DOPA-responsive dystonia-parkinsonismMIM #619911
AD
0
Active trials
1
Pubs (1 yr)
0
P/LP submissions
P/LP missense
LOEUF
Mechanism
Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/IDLDP?content-type=application/json&expand=1

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

IDLDP · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found