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IDDMSSD

Chr 11AD

p21 (RAC1) activated kinase 1

Also known as: IDDMSSD, PAKalpha, alpha-PAK, p65-PAK

This gene encodes a serine/threonine kinase (PAK protein) that links RhoGTPases to cytoskeleton reorganization and nuclear signaling, and regulates cell motility and morphology. Mutations cause intellectual developmental disorder with macrocephaly, seizures, and speech delay. The condition follows an autosomal dominant inheritance pattern.

OMIMResearchSummary from RefSeq, OMIM
AD1 OMIM phenotype
Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/IDDMSSD?content-type=application/json&expand=1

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

IDDMSSD · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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