HSPB3

Chr 5

heat shock protein family B (small) member 3

Also known as: DHMN2C, HMN2C, HMND4, HSPL27

This gene encodes a muscle-specific small heat shock protein. A mutation in this gene is the cause of autosomal dominant distal hereditary motor neuropathy type 2C.[provided by RefSeq, Sep 2010]

ResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtNeuronopathy, distal hereditary motor, autosomal dominant 4
0
Active trials
3
Pubs (1 yr)
P/LP submissions
P/LP missense
1.84
LOEUF
Multiple*
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.84LOEUF
pLI 0.000
Z-score -0.25
OE 1.11 (0.601.84)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
0.04Z-score
OE missense 0.99 (0.821.19)
80 obs / 80.9 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?1.11 (0.601.84)
00.351.4
Missense OE?0.99 (0.821.19)
00.61.4
Synonymous OE?1.11
01.21.6
LoF obs/exp: 6 / 5.4Missense obs/exp: 80 / 80.9Syn Z: -0.49

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

HSPB3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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