HSPB1

Chr 7

heat shock protein family B (small) member 1

Also known as: CMT2F, HEL-S-102, HMN2B, HMND3, HS.76067, HSP27, HSP28, Hsp25

This gene encodes a member of the small heat shock protein (HSP20) family of proteins. In response to environmental stress, the encoded protein translocates from the cytoplasm to the nucleus and functions as a molecular chaperone that promotes the correct folding of other proteins. This protein plays an important role in the differentiation of a wide variety of cell types. Expression of this gene is correlated with poor clinical outcome in multiple human cancers, and the encoded protein may promote cancer cell proliferation and metastasis, while protecting cancer cells from apoptosis. Mutations in this gene have been identified in human patients with Charcot-Marie-Tooth disease and distal hereditary motor neuropathy. [provided by RefSeq, Aug 2017]

ResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtCharcot-Marie-Tooth disease, axonal, type 2F
UniProtNeuronopathy, distal hereditary motor, autosomal dominant 3

Clinical highlights

Gene-disease validity (ClinGen)
Charcot-Marie-Tooth disease axonal type 2F · ADDefinitivesufficient evidence for diagnostic panels
0
Active trials
169
Pubs (1 yr)
P/LP submissions
P/LP missense
1.87
LOEUF
DN
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.87LOEUF
pLI 0.000
Z-score -0.63
OE 1.26 (0.741.87)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
-0.51Z-score
OE missense 1.13 (0.981.30)
136 obs / 120.1 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?1.26 (0.741.87)
00.351.4
Missense OE?1.13 (0.981.30)
00.61.4
Synonymous OE?1.46
01.21.6
LoF obs/exp: 9 / 7.2Missense obs/exp: 136 / 120.1Syn Z: -2.68

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

HSPB1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →