HORMAD1

Chr 1

HORMA domain containing 1

Also known as: CT46, NOHMA

This gene encodes a HORMA domain-containing protein. HORMA domains are involved in chromatin binding and play a role in cell cycle regulation. The encoded protein may play a role in meiosis, and expression of this gene is a potential marker for cancer. A pseudogene of this gene is located on the long arm of chromosome 6. Alternatively spliced transcript variants encoding multiple isoforms have been observed for this gene. [provided by RefSeq, Dec 2010]

ResearchGenerating clinical summary…
LOEUF 0.34
Clinical SummaryHORMAD1
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 0.95). One damaged copy is likely sufficient to cause disease.
📋
ClinVar Variants
1 unique Pathogenic / Likely Pathogenic· 30 VUS of 43 total submissions
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint?
0.34LOEUF
pLI 0.949
Z-score 3.82
OE 0.13 (0.060.34)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint?
1.54Z-score
OE missense 0.69 (0.600.80)
132 obs / 191.9 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.13 (0.060.34)
00.351.4
Missense OE?0.69 (0.600.80)
00.61.4
Synonymous OE?0.89
01.21.6
LoF obs/exp: 3 / 22.6Missense obs/exp: 132 / 191.9Syn Z: 0.72

ClinVar Variant Classifications

43 submitted variants in ClinVar

Classification Summary

Pathogenic1
VUS30
Likely Benign3
Benign1
1
Pathogenic
30
VUS
3
Likely Benign
1
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
1
0
0
0
1
Likely Pathogenic
0
0
0
0
0
VUS
0
30
0
0
30
Likely Benign
0
3
0
0
3
Benign
0
1
0
0
1
Total1340035

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

13 pathogenic / likely-pathogenic (of 18) ClinVar copy-number / structural variants overlap HORMAD1 — these span large chromosomal regions, not the gene specifically, and are excluded from the counts above. Explore in CNV tools →

Protein Context — Lollipop Plot

HORMAD1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →