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HMSN6C

Chr 21AR

pyridoxal kinase

Also known as: C21orf124, C21orf97, HEL-S-1a, HMSN6C, PKH, PNK, PRED79

The protein phosphorylates vitamin B6 to convert it to pyridoxal-5-phosphate, an essential cofactor in intermediary metabolism, and functions as a cytoplasmic homodimer. Mutations cause hereditary motor and sensory neuropathy type VIC with optic atrophy, following autosomal recessive inheritance. This condition affects both the peripheral nervous system and visual pathways.

OMIMResearchSummary from RefSeq, OMIM
AR1 OMIM phenotype
Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/HMSN6C?content-type=application/json&expand=1

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

HMSN6C · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

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Clinical Literature
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Full-Text Mentions
NLP-detected gene mentions in article bodies · via PubTator3
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

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