HMGB2

Chr 4

high mobility group box 2

Also known as: HMG2

This gene encodes a member of the non-histone chromosomal high mobility group protein family. The proteins of this family are chromatin-associated and ubiquitously distributed in the nucleus of higher eukaryotic cells. In vitro studies have demonstrated that this protein is able to efficiently bend DNA and form DNA circles. These studies suggest a role in facilitating cooperative interactions between cis-acting proteins by promoting DNA flexibility. This protein was also reported to be involved in the final ligation step in DNA end-joining processes of DNA double-strand breaks repair and V(D)J recombination. [provided by RefSeq, Jul 2008]

0
Active trials
52
Pubs (1 yr)
0
P/LP submissions
P/LP missense
0.32
LOEUF· LoF intol.
LOF
Mechanism· predicted
Clinical SummaryHMGB2
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 0.95). One damaged copy is likely sufficient to cause disease.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.32LOEUF
pLI 0.951
Z-score 2.85
OE 0.00 (0.000.32)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
1.61Z-score
OE missense 0.58 (0.470.71)
66 obs / 114.5 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.00 (0.000.32)
00.351.4
Missense OE0.58 (0.470.71)
00.61.4
Synonymous OE1.24
01.21.6
LoF obs/exp: 0 / 9.5Missense obs/exp: 66 / 114.5Syn Z: -1.20
DN
0.3892th %ile
GOF
0.2795th %ile
LOF
0.66top 25%

The highest-scoring mechanism for this gene is loss-of-function (haploinsufficiency).

LOFprediction above median · LOEUF 0.32

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

HMGB2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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