HLA-DQA1

Chr 6

major histocompatibility complex, class II, DQ alpha 1

Also known as: CELIAC1, DQ-A1, DQA1, HLA-DQA, HLA-DQA1*

HLA-DQA1 belongs to the HLA class II alpha chain paralogues. The class II molecule is a heterodimer consisting of an alpha (DQA) and a beta chain (DQB), both anchored in the membrane. It plays a central role in the immune system by presenting peptides derived from extracellular proteins. Class II molecules are expressed in antigen presenting cells (APC: B Lymphocytes, dendritic cells, macrophages). The alpha chain is approximately 33-35 kDa. It is encoded by 5 exons; exon 1 encodes the leader peptide, exons 2 and 3 encode the two extracellular domains, and exon 4 encodes the transmembrane domain and the cytoplasmic tail. Within the DQ molecule both the alpha chain and the beta chain contain the polymorphisms specifying the peptide binding specificities, resulting in up to four different molecules. Typing for these polymorphisms is routinely done for bone marrow transplantation. [provided by RefSeq, Jul 2008]

GeneReviewsResearchGenerating clinical summary…
1
Active trials
198
Pubs (1 yr)
P/LP submissions
P/LP missense
0.97
LOEUF
Multiple*
Mechanism· predicted
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GeneReview available — HLA-DQA1
Authoritative clinical overview · Recommended first read
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Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.97LOEUF
pLI 0.024
Z-score 1.64
OE 0.42 (0.210.97)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
1.63Z-score
OE missense 0.60 (0.490.72)
77 obs / 129.1 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.42 (0.210.97)
00.351.4
Missense OE?0.60 (0.490.72)
00.61.4
Synonymous OE?0.72
01.21.6
LoF obs/exp: 4 / 9.4Missense obs/exp: 77 / 129.1Syn Z: 1.53

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

HLA-DQA1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.