HLA-DMB

Chr 6

major histocompatibility complex, class II, DM beta

Also known as: D6S221E, RING7

HLA-DMB belongs to the HLA class II beta chain paralogues. This class II molecule is a heterodimer consisting of an alpha (DMA) and a beta (DMB) chain, both anchored in the membrane. It is located in intracellular vesicles. DM plays a central role in the peptide loading of MHC class II molecules by helping to release the CLIP (class II-associated invariant chain peptide) molecule from the peptide binding site. Class II molecules are expressed in antigen presenting cells (APC: B lymphocytes, dendritic cells, macrophages). The beta chain is approximately 26-28 kDa and its gene contains 6 exons. Exon one encodes the leader peptide, exons 2 and 3 encode the two extracellular domains, exon 4 encodes the transmembrane domain and exon 5 encodes the cytoplasmic tail. [provided by RefSeq, Jul 2008]

OMIMResearchGenerating clinical summary…
0
Active trials
14
Pubs (1 yr)
P/LP submissions
P/LP missense
0.98
LOEUF
Multiple*
Mechanism· predicted

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.98LOEUF
pLI 0.002
Z-score 1.63
OE 0.49 (0.270.98)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
1.59Z-score
OE missense 0.63 (0.530.75)
89 obs / 142.3 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.49 (0.270.98)
00.351.4
Missense OE?0.63 (0.530.75)
00.61.4
Synonymous OE?0.97
01.21.6
LoF obs/exp: 6 / 12.1Missense obs/exp: 89 / 142.3Syn Z: 0.18

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

HLA-DMB · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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