HHLA1

Chr 8

HHLA1 neighbor of OC90

Also known as: PLA2L

The HHLA1 protein is predicted to be located in the extracellular region, but its specific function remains unclear. Clinical associations with human disease have not been established for mutations in this gene. The gene shows tolerance to loss-of-function variation (pLI near zero, LOEUF 1.222), suggesting it may not be essential for normal development.

Summary from RefSeq
Research Assistant →
0
Active trials
0
Pubs (1 yr)
55
P/LP submissions
0%
P/LP missense
1.22
LOEUF
Mechanism
Clinical SummaryHHLA1
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
55 unique Pathogenic / Likely Pathogenic· 98 VUS of 167 total submissions
Some data sources returned errors (1)

opentargets: Error: Internal server error

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.22LOEUF
pLI 0.000
Z-score 0.66
OE 0.86 (0.621.22)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.71Z-score
OE missense 0.88 (0.790.98)
247 obs / 280.2 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.86 (0.621.22)
00.351.4
Missense OE0.88 (0.790.98)
00.61.4
Synonymous OE0.91
01.21.6
LoF obs/exp: 23 / 26.7Missense obs/exp: 247 / 280.2Syn Z: 0.69

ClinVar Variant Classifications

167 submitted variants in ClinVar

Classification Summary

Pathogenic54
Likely Pathogenic1
VUS98
Likely Benign9
54
Pathogenic
1
Likely Pathogenic
98
VUS
9
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
54
0
54
Likely Pathogenic
0
0
1
0
1
VUS
0
85
13
0
98
Likely Benign
0
8
0
1
9
Benign
0
0
0
0
0
Total093681162

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

HHLA1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 1 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found