HASPIN

Chr 17

histone H3 associated protein kinase

Also known as: GSG2

HASPIN encodes a serine/threonine kinase that phosphorylates histone H3 at threonine-3 during mitosis and positions the chromosomal passenger complex at centromeres to ensure proper chromosome segregation and cell cycle progression. Mutations cause autosomal recessive developmental delay with seizures and dysmorphic features. The gene shows tolerance to loss-of-function variants, consistent with the recessive inheritance pattern observed clinically.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 1.01
Clinical SummaryHASPIN
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.01LOEUF
pLI 0.000
Z-score 1.53
OE 0.63 (0.411.01)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.66Z-score
OE missense 0.91 (0.840.99)
412 obs / 451.2 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.63 (0.411.01)
00.351.4
Missense OE0.91 (0.840.99)
00.61.4
Synonymous OE1.04
01.21.6
LoF obs/exp: 13 / 20.5Missense obs/exp: 412 / 451.2Syn Z: -0.43

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

HASPIN · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Full-Text Mentions
NLP-detected gene mentions in article bodies · via PubTator3
PubTator3
Top 5 full-text resultsSearch PubTator3 ↗