HABP2

Chr 10

hyaluronan binding protein 2

Also known as: FSAP, HABP, HGFAL, NMTC5, PHBP, PHBSP

This gene encodes a member of the peptidase S1 family of serine proteases. The encoded preproprotein is secreted by hepatocytes and proteolytically processed to generate heavy and light chains that form the mature heterodimer. Further autoproteolysis leads to smaller, inactive peptides. This extracellular protease binds hyaluronic acid and may play a role in the coagulation and fibrinolysis systems. Mutations in this gene are associated with nonmedullary thyroid cancer and susceptibility to venous thromboembolism. Alternative splicing results in multiple transcript variants, at least one of which encodes a preproprotein that is proteolytically processed. [provided by RefSeq, Jan 2016]

ResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtThyroid cancer, non-medullary, 5
0
Active trials
12
Pubs (1 yr)
P/LP submissions
P/LP missense
1.20
LOEUF
Mechanism
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.20LOEUF
pLI 0.000
Z-score 0.69
OE 0.86 (0.631.20)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
-1.43Z-score
OE missense 1.23 (1.131.34)
385 obs / 313.5 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?0.86 (0.631.20)
00.351.4
Missense OE?1.23 (1.131.34)
00.61.4
Synonymous OE?1.16
01.21.6
LoF obs/exp: 25 / 29.0Missense obs/exp: 385 / 313.5Syn Z: -1.34

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

HABP2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →