H6PD

Chr 1

hexose-6-phosphate dehydrogenase/glucose 1-dehydrogenase

Also known as: CORTRD1, G6PDH, GDH, H6PDH

There are 2 forms of glucose-6-phosphate dehydrogenase. G form is X-linked and H form, encoded by this gene, is autosomally linked. This H form shows activity with other hexose-6-phosphates, especially galactose-6-phosphate, whereas the G form is specific for glucose-6-phosphate. Both forms are present in most tissues, but H form is not found in red cells. [provided by RefSeq, Jul 2008]

ResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtCortisone reductase deficiency 1
0
Active trials
20
Pubs (1 yr)
P/LP submissions
P/LP missense
0.94
LOEUF
Multiple*
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.94LOEUF
pLI 0.000
Z-score 1.80
OE 0.63 (0.430.94)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
-1.13Z-score
OE missense 1.15 (1.071.23)
549 obs / 479.2 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?0.63 (0.430.94)
00.351.4
Missense OE?1.15 (1.071.23)
00.61.4
Synonymous OE?1.15
01.21.6
LoF obs/exp: 17 / 27.1Missense obs/exp: 549 / 479.2Syn Z: -1.74

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

H6PD · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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