H2AB3

Chr X

H2A.B variant histone 3

Also known as: H2A.B.1, H2A.Bbd, H2ABBD, H2AFB, H2AFB3

H2AB3 encodes an atypical histone H2A protein that replaces conventional H2A in some nucleosomes and is associated with active transcription and mRNA processing, forming less rigid nucleosomes that are enriched in actively transcribed genes and required for mRNA splicing. Currently, no well-established human diseases have been definitively linked to H2AB3 mutations in the medical literature. The gene is located on chromosome X as part of a repeated region.

OMIMResearchSummary from RefSeq, UniProt
DNmechanism
Some data sources returned errors (1)

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

DN
0.6258th %ile
GOF
0.4579th %ile
LOF
0.3164th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

H2AB3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found