H2AB2

Chr X

H2A.B variant histone 2

Also known as: H2A.B.1, H2A.Bbd, H2AFB2

Histones are basic nuclear proteins that are responsible for the nucleosome structure of the chromosomal fiber in eukaryotes. Nucleosomes consist of approximately 146 bp of DNA wrapped around a histone octamer composed of pairs of each of the four core histones (H2A, H2B, H3, and H4). The chromatin fiber is further compacted through the interaction of a linker histone, H1, with the DNA between the nucleosomes to form higher order chromatin structures. This gene encodes a replication-independent histone that is a member of the histone H2A family. This gene is part of a region that is repeated three times on chromosome X, once in intron 22 of the F8 gene and twice closer to the Xq telomere. This record represents the middle copy. [provided by RefSeq, Oct 2015]

124
ClinVar variants
114
Pathogenic / LP
pLI score
0
Active trials
Clinical SummaryH2AB2
📋
ClinVar Variants
114 Pathogenic / Likely Pathogenic· 9 VUS of 124 total submissions
Some data sources returned errors (1)

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

124 submitted variants in ClinVar

Classification Summary

Pathogenic110
Likely Pathogenic4
VUS9
Likely Benign1
110
Pathogenic
4
Likely Pathogenic
9
VUS
1
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories· variant type breakdown unavailable

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
110
Likely Pathogenic
4
VUS
9
Likely Benign
1
Benign
0
Total124

Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

H2AB2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

OMIM — Genotype-Phenotype Relationships

1 OMIM entry