GTF2F2

Chr 13

general transcription factor IIF subunit 2

Also known as: BTF4, RAP30, TF2F2, TFIIF

The protein functions as part of the TFIIF complex, a general transcription initiation factor that binds to RNA polymerase II and helps recruit it to the initiation complex for gene transcription. Mutations in GTF2F2 cause neurodevelopmental disorder with seizures and brain atrophy, inherited in an autosomal recessive pattern. The gene is not highly constrained against loss-of-function variants, which is consistent with the recessive inheritance pattern observed in affected patients.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 0.85
Clinical SummaryGTF2F2
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.85LOEUF
pLI 0.000
Z-score 2.05
OE 0.49 (0.290.85)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
1.29Z-score
OE missense 0.67 (0.560.81)
82 obs / 122.0 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.49 (0.290.85)
00.351.4
Missense OE0.67 (0.560.81)
00.61.4
Synonymous OE1.11
01.21.6
LoF obs/exp: 9 / 18.5Missense obs/exp: 82 / 122.0Syn Z: -0.58

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

GTF2F2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC