GTF2A1L

Chr 2

general transcription factor IIA subunit 1 like

Also known as: ALF

The protein functions as a testis-specific transcription factor that binds DNA with other factors to enable mRNA transcription. This gene is extremely tolerant to loss-of-function variation (very low pLI score), and no established human diseases have been definitively associated with GTF2A1L mutations. Given its testis-specific expression pattern, any potential clinical manifestations would likely involve male reproductive function rather than neurological phenotypes.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
1
Pubs (1 yr)
12
P/LP submissions
0%
P/LP missense
1.27
LOEUF
Mechanism
Clinical SummaryGTF2A1L
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
12 unique Pathogenic / Likely Pathogenic· 45 VUS of 61 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.27LOEUF
pLI 0.000
Z-score 0.61
OE 0.86 (0.591.27)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-1.36Z-score
OE missense 1.24 (1.131.36)
310 obs / 249.7 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.86 (0.591.27)
00.351.4
Missense OE1.24 (1.131.36)
00.61.4
Synonymous OE1.33
01.21.6
LoF obs/exp: 18 / 21.0Missense obs/exp: 310 / 249.7Syn Z: -2.45

ClinVar Variant Classifications

61 submitted variants in ClinVar

Classification Summary

Pathogenic11
Likely Pathogenic1
VUS45
Likely Benign3
Benign1
11
Pathogenic
1
Likely Pathogenic
45
VUS
3
Likely Benign
1
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
11
0
11
Likely Pathogenic
0
0
1
0
1
VUS
0
36
9
0
45
Likely Benign
0
1
2
0
3
Benign
0
0
1
0
1
Total03724061

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

GTF2A1L · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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