GRIP1

Chr 12AR

glutamate receptor interacting protein 1

Also known as: FRASRS3, GRIP

The encoded protein is a scaffold protein that binds to and mediates trafficking and membrane organization of transmembrane proteins, including controlling AMPA receptor fate and endosomal sorting in neurons. Mutations cause Fraser syndrome 3, inherited in an autosomal recessive pattern. The gene shows significant constraint against loss-of-function variants (LOEUF 0.356), suggesting loss-of-function mutations are poorly tolerated.

OMIMResearchSummary from RefSeq, OMIM, UniProt
LOFmechanismARLOEUF 0.361 OMIM phenotype
Clinical SummaryGRIP1
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Gene-Disease Validity (ClinGen)
Fraser syndrome 3 · ARDefinitive

Definitive — sufficient evidence for diagnostic panels

Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.51) — some intolerance to loss-of-function variants.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.36LOEUF
pLI 0.508
Z-score 5.34
OE 0.22 (0.140.36)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
1.58Z-score
OE missense 0.82 (0.760.88)
478 obs / 585.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.22 (0.140.36)
00.351.4
Missense OE0.82 (0.760.88)
00.61.4
Synonymous OE1.04
01.21.6
LoF obs/exp: 12 / 54.6Missense obs/exp: 478 / 585.7Syn Z: -0.50
Curated Mechanism (G2P)Gene2Phenotype (DDG2P) ↗
strongGRIP1-related Fraser syndromeLOFAR

Predictions shown for reference only — model trained on dominant genes, not applicable to AR conditions.

DN
0.5869th %ile
GOF
0.6541th %ile
LOF
0.57top 25%

The Badonyi & Marsh prediction model was trained exclusively on dominant disease genes. Predictions are not reliable for genes with autosomal recessive inheritance and are shown at reduced opacity for reference only.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

GRIP1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 5 results · since 2015Search PubMed ↗