GOLGA8N

Chr 15

golgin A8 family member N

This protein is predicted to be involved in Golgi organization and is located in the Golgi apparatus, specifically in the cis-Golgi network and cisterna membranes. Currently, no human diseases have been definitively associated with mutations in GOLGA8N. The gene shows moderate tolerance to loss-of-function variants (pLI = 0.29, LOEUF = 1.22), suggesting it may not be essential for normal development.

Summary from RefSeq
Research Assistant →
0
Active trials
0
Pubs (1 yr)
47
P/LP submissions
P/LP missense
1.22
LOEUF
Multiple*
Mechanism· predicted
Clinical SummaryGOLGA8N
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.26) despite low pLI — interpret in context.
📋
ClinVar Variants
47 unique Pathogenic / Likely Pathogenic· 13 VUS of 63 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.22LOEUF
pLI 0.286
Z-score 1.34
OE 0.26 (0.091.22)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.19Z-score
OE missense 1.10 (0.831.50)
30 obs / 27.2 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.26 (0.091.22)
00.351.4
Missense OE1.10 (0.831.50)
00.61.4
Synonymous OE1.02
01.21.6
LoF obs/exp: 1 / 3.8Missense obs/exp: 30 / 27.2Syn Z: -0.04
DN
0.73top 25%
GOF
0.74top 25%
LOF
0.2582th %ile

This gene has evidence for multiple mechanisms of pathogenicity (gain-of-function and dominant-negative). Both the Badonyi & Marsh prediction and the broader genomic evidence point to gain-of-function as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

GOFprediction above median
DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

63 submitted variants in ClinVar

Classification Summary

Pathogenic43
Likely Pathogenic4
VUS13
Benign1
Conflicting2
43
Pathogenic
4
Likely Pathogenic
13
VUS
1
Benign
2
Conflicting

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories· variant type breakdown unavailable

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
43
Likely Pathogenic
4
VUS
13
Likely Benign
0
Benign
1
Conflicting
2
Total63

Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

GOLGA8N · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found