GNMT

Chr 6

glycine N-methyltransferase

Also known as: HEL-S-182mP

The protein encoded by this gene is an enzyme that catalyzes the conversion of S-adenosyl-L-methionine (along with glycine) to S-adenosyl-L-homocysteine and sarcosine. This protein is found in the cytoplasm and acts as a homotetramer. Defects in this gene are a cause of GNMT deficiency (hypermethioninemia). Alternative splicing results in multiple transcript variants. Naturally occurring readthrough transcription occurs between the upstream CNPY3 (canopy FGF signaling regulator 3) gene and this gene and is represented with GeneID:107080644. [provided by RefSeq, Jan 2016]

ResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtGlycine N-methyltransferase deficiency

Clinical highlights

Gene-disease validity (ClinGen)
glycine N-methyltransferase deficiency · ARLimitednot for standalone diagnostic reporting
0
Active trials
23
Pubs (1 yr)
P/LP submissions
P/LP missense
0.95
LOEUF
DN
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.95LOEUF
pLI 0.003
Z-score 1.70
OE 0.48 (0.260.95)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
0.35Z-score
OE missense 0.92 (0.811.05)
159 obs / 172.1 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.48 (0.260.95)
00.351.4
Missense OE?0.92 (0.811.05)
00.61.4
Synonymous OE?0.80
01.21.6
LoF obs/exp: 6 / 12.5Missense obs/exp: 159 / 172.1Syn Z: 1.38

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

GNMT · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →