GLYCTK

Chr 3AR

glycerate kinase

Also known as: HBEBP2, HBEBP4, HBeAgBP4A

This locus encodes a member of the glycerate kinase type-2 family. The encoded enzyme catalyzes the phosphorylation of (R)-glycerate and may be involved in serine degradation and fructose metabolism. Decreased activity of the encoded enzyme may be associated with the disease D-glyceric aciduria. Alternatively spliced transcript variants have been described. [provided by RefSeq, Jan 2009]

OMIMResearchGenerating clinical summary…
DNmechanismARLOEUF 1.601 OMIM phenotype
Clinical SummaryGLYCTK
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Gene-Disease Validity (ClinGen)
D-glyceric aciduria · ARModerate

Moderate evidence — consider for supplementary testing

Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.60LOEUF
pLI 0.000
Z-score -0.17
OE 1.05 (0.701.60)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
-0.23Z-score
OE missense 1.04 (0.951.13)
333 obs / 321.5 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?1.05 (0.701.60)
00.351.4
Missense OE?1.04 (0.951.13)
00.61.4
Synonymous OE?1.05
01.21.6
LoF obs/exp: 15 / 14.3Missense obs/exp: 333 / 321.5Syn Z: -0.50

This gene — mechanism propensity

DN
0.6357th %ile
GOF
0.4382th %ile
LOF
0.3550th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

GLYCTK · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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