GLI1

Chr 12

GLI family zinc finger 1

Also known as: GLI, PAPA8, PPD1

This gene encodes a member of the Kruppel family of zinc finger proteins. The encoded transcription factor is activated by the sonic hedgehog signal transduction cascade and regulates stem cell proliferation. The activity and nuclear localization of this protein is negatively regulated by p53 in an inhibitory loop. Multiple transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, May 2009]

ResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtPolydactyly, postaxial, A8
UniProtPolydactyly, preaxial 1
2
Active trials
368
Pubs (1 yr)
P/LP submissions
P/LP missense
0.92
LOEUF
DN
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.92LOEUF
pLI 0.000
Z-score 1.94
OE 0.67 (0.490.92)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
1.08Z-score
OE missense 0.88 (0.820.94)
580 obs / 657.9 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.67 (0.490.92)
00.351.4
Missense OE?0.88 (0.820.94)
00.61.4
Synonymous OE?0.92
01.21.6
LoF obs/exp: 27 / 40.3Missense obs/exp: 580 / 657.9Syn Z: 0.99

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

GLI1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.