GJA8

Chr 1

gap junction protein alpha 8

Also known as: CAE, CAE1, CTRCT1, CX50, CZP1, MP70

This gene encodes a transmembrane connexin protein that is necessary for lens growth and maturation of lens fiber cells. The encoded protein is a component of gap junction channels and functions in a calcium and pH-dependent manner. Mutations in this gene have been associated with zonular pulverulent cataracts, nuclear progressive cataracts, and cataract-microcornea syndrome. [provided by RefSeq, Dec 2009]

ResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtCataract 1, multiple types
0
Active trials
15
Pubs (1 yr)
P/LP submissions
P/LP missense
1.00
LOEUF
Multiple*
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.00LOEUF
pLI 0.002
Z-score 1.58
OE 0.51 (0.281.00)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
-0.20Z-score
OE missense 1.03 (0.941.14)
270 obs / 261.0 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?0.51 (0.281.00)
00.351.4
Missense OE?1.03 (0.941.14)
00.61.4
Synonymous OE?1.18
01.21.6
LoF obs/exp: 6 / 11.9Missense obs/exp: 270 / 261.0Syn Z: -1.57

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

GJA8 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →