GJA5

Chr 1

gap junction protein alpha 5

Also known as: ATFB11, CX40

This gene is a member of the connexin gene family. The encoded protein is a component of gap junctions, which are composed of arrays of intercellular channels that provide a route for the diffusion of low molecular weight materials from cell to cell. Mutations in this gene may be associated with atrial fibrillation. Alternatively spliced transcript variants encoding the same isoform have been described. [provided by RefSeq, Jul 2008]

ResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtAtrial standstill 1
UniProtAtrial fibrillation, familial, 11

Clinical highlights

Gene-disease validity (ClinGen)
congenital heart disease · ADDisputedevidence questions this relationship
0
Active trials
10
Pubs (1 yr)
P/LP submissions
P/LP missense
0.81
LOEUF
Multiple*
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.81LOEUF
pLI 0.018
Z-score 2.04
OE 0.39 (0.200.81)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
1.11Z-score
OE missense 0.79 (0.690.89)
169 obs / 214.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.39 (0.200.81)
00.351.4
Missense OE?0.79 (0.690.89)
00.61.4
Synonymous OE?0.95
01.21.6
LoF obs/exp: 5 / 12.9Missense obs/exp: 169 / 214.8Syn Z: 0.33

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

GJA5 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →