GDF2

Chr 10

growth differentiation factor 2

Also known as: BMP-9, BMP9, HHT5

This gene encodes a secreted ligand of the TGF-beta (transforming growth factor-beta) superfamily of proteins. Ligands of this family bind various TGF-beta receptors leading to recruitment and activation of SMAD family transcription factors that regulate gene expression. The encoded preproprotein is proteolytically processed to generate each subunit of the disulfide-linked homodimer. This protein regulates cartilage and bone development, angiogenesis and differentiation of cholinergic central nervous system neurons. Mutations in this gene are associated with hereditary hemorrhagic telangiectasia. [provided by RefSeq, Jul 2016]

GeneReviewsResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtTelangiectasia, hereditary hemorrhagic, 5

Clinical highlights

Gene-disease validity (ClinGen)
pulmonary arterial hypertension · ADDefinitivesufficient evidence for diagnostic panels2 gene-disease associations curated in total
0
Active trials
22
Pubs (1 yr)
P/LP submissions
P/LP missense
0.98
LOEUF
DN
Mechanism· predicted
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GeneReview available — GDF2
Authoritative clinical overview · Recommended first read
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Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.98LOEUF
pLI 0.002
Z-score 1.63
OE 0.49 (0.270.98)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
0.46Z-score
OE missense 0.92 (0.831.02)
239 obs / 259.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.49 (0.270.98)
00.351.4
Missense OE?0.92 (0.831.02)
00.61.4
Synonymous OE?1.24
01.21.6
LoF obs/exp: 6 / 12.1Missense obs/exp: 239 / 259.8Syn Z: -2.08

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

GDF2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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