GBGT1

Chr 9

globoside alpha-1,3-N-acetylgalactosaminyltransferase 1 (FORS blood group)

Also known as: A3GALNT, FS, UNQ2513

This protein is a glycosyltransferase involved in glycosphingolipid metabolism, though it has lost the ability to synthesize Forssman glycolipid antigen and its current functional role remains unclear. The gene shows very low constraint against loss-of-function variants, indicating that complete loss of protein function is likely well-tolerated in humans. No established human diseases have been definitively linked to mutations in this gene.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 1.59
Clinical SummaryGBGT1
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.59LOEUF
pLI 0.000
Z-score -0.14
OE 1.04 (0.691.59)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.04Z-score
OE missense 0.99 (0.891.11)
215 obs / 216.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE1.04 (0.691.59)
00.351.4
Missense OE0.99 (0.891.11)
00.61.4
Synonymous OE1.00
01.21.6
LoF obs/exp: 15 / 14.4Missense obs/exp: 215 / 216.8Syn Z: 0.02

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

GBGT1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →