GARNL3

Chr 9

GTPase activating Rap/RanGAP domain like 3

Also known as: bA356B19.1

The protein is predicted to function as a GTPase activator, regulating small GTPase-mediated signal transduction pathways. GARNL3 is highly constrained against loss-of-function variants (pLI ~1.0, LOEUF 0.50), suggesting that mutations in this gene would likely cause severe developmental disorders, though specific associated phenotypes have not yet been established in the literature. The inheritance pattern for GARNL3-related conditions remains to be determined.

ResearchSummary from RefSeq
LOEUF 0.50
Clinical SummaryGARNL3
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.35) despite low pLI — interpret in context.
📋
ClinVar Variants
36 unique Pathogenic / Likely Pathogenic· 104 VUS of 167 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.50LOEUF
pLI 0.000
Z-score 4.62
OE 0.35 (0.240.50)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
2.02Z-score
OE missense 0.76 (0.700.82)
435 obs / 571.0 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.35 (0.240.50)
00.351.4
Missense OE0.76 (0.700.82)
00.61.4
Synonymous OE1.04
01.21.6
LoF obs/exp: 20 / 58.0Missense obs/exp: 435 / 571.0Syn Z: -0.51

ClinVar Variant Classifications

167 submitted variants in ClinVar

Classification Summary

Pathogenic34
Likely Pathogenic2
VUS104
Likely Benign5
34
Pathogenic
2
Likely Pathogenic
104
VUS
5
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
34
0
34
Likely Pathogenic
0
1
1
0
2
VUS
0
103
1
0
104
Likely Benign
0
3
1
1
5
Benign
0
0
0
0
0
Total0107371145

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

GARNL3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC