GALNTL6

Chr 4

polypeptide N-acetylgalactosaminyltransferase like 6

Also known as: GALNACT20, GALNT17, GalNAc-T6L

GALNTL6 encodes a polypeptide N-acetylgalactosaminyltransferase that catalyzes the initial step in O-linked oligosaccharide biosynthesis by transferring N-acetyl-D-galactosamine to serine or threonine residues on proteins in the Golgi apparatus. The gene shows low constraint against loss-of-function variants (LOEUF 0.823), and no definitive disease associations have been established for this gene. The inheritance pattern and clinical phenotypes associated with GALNTL6 mutations remain to be determined.

OMIMResearchSummary from RefSeq, UniProt
MultiplemechanismLOEUF 0.82
Clinical SummaryGALNTL6
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.82LOEUF
pLI 0.000
Z-score 2.37
OE 0.56 (0.390.82)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
2.14Z-score
OE missense 0.68 (0.610.75)
234 obs / 346.0 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.56 (0.390.82)
00.351.4
Missense OE0.68 (0.610.75)
00.61.4
Synonymous OE1.04
01.21.6
LoF obs/exp: 19 / 33.9Missense obs/exp: 234 / 346.0Syn Z: -0.33
DN
0.6841th %ile
GOF
0.6637th %ile
LOF
0.2679th %ile

This gene has evidence for multiple mechanisms of pathogenicity (dominant-negative and gain-of-function). Both the Badonyi & Marsh prediction and the broader genomic evidence point to dominant-negative as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

DNprediction above median
GOFprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

GALNTL6 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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