GALNT17

Chr 7

polypeptide N-acetylgalactosaminyltransferase 17

Also known as: GALNACT17, GALNT20, GALNTL3, GalNAc-T17, GalNAc-T19, GalNAc-T5L, WBSCR17

This gene encodes an N-acetylgalactosaminyltransferase that catalyzes the initial step in O-linked oligosaccharide biosynthesis by transferring N-acetyl-D-galactosamine to serine or threonine residues on protein receptors. The gene is highly constrained against loss-of-function variants and is located near the Williams-Beuren syndrome deletion region at 7q11.23, but specific disease associations with GALNT17 mutations have not been established. The protein may contribute to membrane trafficking processes.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 0.49
Clinical SummaryGALNT17
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.26) despite low pLI — interpret in context.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.49LOEUF
pLI 0.117
Z-score 3.57
OE 0.26 (0.150.49)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
2.44Z-score
OE missense 0.65 (0.580.72)
243 obs / 376.2 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.26 (0.150.49)
00.351.4
Missense OE0.65 (0.580.72)
00.61.4
Synonymous OE0.89
01.21.6
LoF obs/exp: 7 / 27.0Missense obs/exp: 243 / 376.2Syn Z: 1.05

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

GALNT17 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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