GADD45G

Chr 9

growth arrest and DNA damage inducible gamma

Also known as: CR6, DDIT2, GADD45gamma, GRP17

The protein mediates activation of stress-responsive MTK1/MEKK4 MAPKKK and is involved in the regulation of growth and apoptosis in response to environmental stresses. Mutations in this gene cause autosomal recessive neurodevelopmental disorder with seizures, microcephaly, and brain atrophy. The gene shows moderate constraint against loss-of-function variants (LOEUF 0.719), and the associated disorder involves the central nervous system with early-onset developmental abnormalities.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 0.72
Clinical SummaryGADD45G
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.55) — some intolerance to loss-of-function variants.
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ClinVar Variants
28 unique Pathogenic / Likely Pathogenic· 11 VUS of 50 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.72LOEUF
pLI 0.553
Z-score 2.02
OE 0.15 (0.050.72)
Moderately constrained

Typical tolerance to LoF variation

Missense Constraint
2.00Z-score
OE missense 0.42 (0.330.55)
40 obs / 94.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.15 (0.050.72)
00.351.4
Missense OE0.42 (0.330.55)
00.61.4
Synonymous OE1.07
01.21.6
LoF obs/exp: 1 / 6.6Missense obs/exp: 40 / 94.7Syn Z: -0.37

ClinVar Variant Classifications

50 submitted variants in ClinVar

Classification Summary

Pathogenic23
Likely Pathogenic5
VUS11
Likely Benign2
Benign2
23
Pathogenic
5
Likely Pathogenic
11
VUS
2
Likely Benign
2
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
23
0
23
Likely Pathogenic
0
0
5
0
5
VUS
0
8
3
0
11
Likely Benign
0
0
2
0
2
Benign
0
1
1
0
2
Total0934043

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

GADD45G · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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