GAD2

Chr 10

glutamate decarboxylase 2

Also known as: GAD65

This gene encodes one of several forms of glutamic acid decarboxylase, identified as a major autoantigen in insulin-dependent diabetes. The enzyme encoded is responsible for catalyzing the production of gamma-aminobutyric acid from L-glutamic acid. A pathogenic role for this enzyme has been identified in the human pancreas since it has been identified as an autoantibody and an autoreactive T cell target in insulin-dependent diabetes. This gene may also play a role in the stiff man syndrome. Alternative splicing results in multiple transcript variants that encode the same protein. [provided by RefSeq, Oct 2008]

ResearchGenerating clinical summary…

Clinical highlights

Interpreting a novel variant
This gene is strongly intolerant of loss-of-function variation in the population, so LoF variants warrant close attention. No curated mechanism annotation is available — see the mechanism card for the computational prediction and its caveats.Based on population constraint only.
4
Active trials
92
Pubs (1 yr)
P/LP submissions
P/LP missense
0.37
LOEUF
Mechanism
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint?
0.37LOEUF
pLI 0.751
Z-score 4.42
OE 0.20 (0.110.37)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint?
1.53Z-score
OE missense 0.77 (0.690.85)
258 obs / 337.0 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.20 (0.110.37)
00.351.4
Missense OE?0.77 (0.690.85)
00.61.4
Synonymous OE?1.00
01.21.6
LoF obs/exp: 7 / 35.4Missense obs/exp: 258 / 337.0Syn Z: 0.03

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

GAD2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.